Articles

SUCCESSFUL TREATMENT OF PLASTIC BRONCHITIS WITH LOW FAT DIET AND SUBSEQUENT THORACIC DUCT LIGATION IN CHILD WITH FONTAN PHYSIOLOGY

Authors: , , , , , , , , , , ,

Abstract

Plastic bronchitis is a rare condition characterized by the formation and expectoration of long, branching bronchial casts that develop in the tracheobronchial tree and cause airway obstruction. Plastic bronchitis has become increasingly recognized as a feared complication of the Fontan operation with a mortality of up to 50%. We report an 11 year old boy who developed severe plastic bronchitis following Fontan repair and the successful long-term control of cast formation utilizing a low-fat diet and subsequent thoracic duct ligation.

Keywords: plastic bronchitis, Fontan procedure, chyloptysis, low fat diet, thoracic duct ligation, lymphscintigram

How to Cite: Parikh, K. , Witte, M. , Samson, R. , Teodori, M. , Carpenter, J. , Lowe, M. , Morgan, W. , Hardin, C. , Brown, M. , Naughton, Y. , Sinha, S. & Barber, B. (2012) “SUCCESSFUL TREATMENT OF PLASTIC BRONCHITIS WITH LOW FAT DIET AND SUBSEQUENT THORACIC DUCT LIGATION IN CHILD WITH FONTAN PHYSIOLOGY”, Lymphology. 45(2).